Familial occurrence of pulmonary alveolar microlithiasis in 3 siblings.
نویسنده
چکیده
Pulmonary alveolar microlithiasis (PAM) is a rare disease of unknown etiology characterized by intra-alveolar calcium deposits. More than 500 cases were reported in the literature. The disorder affects people at every age beginning from the early childhood. It occurs probably as a result of autosomal recessive transmission. Familial occurrence is often found with family history of the disease being present in up to 50% of the reported cases. We report PAM in 3 siblings.
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ورودعنوان ژورنال:
- Saudi medical journal
دوره 27 2 شماره
صفحات -
تاریخ انتشار 2006